UKGTN and Commissioning

 
 
 

UKGTN Approved Testing

The UKGTN assesses whether providing a test as an NHS service is likely to be of benefit to patients. Approved tests has been evaluated for clinical validity and utility.

All approved tests are listed in the NHS Directory of Molecular Genetic Testing

Not all requests for new tests are accepted by the UKGTN. There can be a variety of reasons for this, including: unclear scientific understanding; the test is still in the research phase; or the test does not add anything new in the diagnosis or management of the patient.

New tests approved by GenCAG in 2007 for services in 2008/9

DISEASE GENE  
NAME OMIM GENE OMIM  Laboratory
AICARDI-GOUTIERES SYNDROME 1; AGS1 225750 3-PRIME @REPAIR EXONUCLEASE 1; TREX1 606609 Leeds regional molecular genetics laboratory (Diagnostic)
AICARDI-GOUTIERES SYNDROME 2; AGS2 610181 RIBONUCLEASE H2, SUBUNIT B; RNASEH2B 610326 Leeds regional molecular genetics laboratory (Diagnostic)
AICARDI-GOUTIERES SYNDROME 3; AGS3 610329 RIBONUCLEASE H2, SUBUNIT C; RNASEH2C 610330 Leeds regional molecular genetics laboratory (Diagnostic)
AICARDI-GOUTIERES SYNDROME 4; AGS4 610333 RIBONUCLEASE H2, SUBUNIT A; RNASEH2A 606034 Leeds regional molecular genetics laboratory (Diagnostic)
AICARDI-GOUTIERES SYNDROME 5; AGS5 610905 3-PRIME @REPAIR EXONUCLEASE 1; TREX1 606609 Leeds regional molecular genetics laboratory (Diagnostic)
CEREBRAL CAVERNOUS MALFORMATIONS; CCM 116860 KRIT 1, ANKYRIN REPEAT CONTAINING; KRIT1 604214 Dundee regional molecular genetics laboratory (Diagnostic)
CEREBRAL CAVERNOUS MALFORMATION 2; CCM2 603284
PROGRAMMED CELL DEATH 10; PDCD10 603285
Charcot Marie Tooth disease, demyelinating, type 1D; CMT1D 607678 Early Growth Response 2; EGR2 129010 Bristol regional molecular genetics laboratory (Diagnostic)
CHARCOT-MARIE-TOOTH DISEASE, AXONAL, TYPE 2A2; CMT2A2 609260 MITOFUSIN 2; MFN2 608507 London Institute of Neurology molecular genetics laboratory (Diagnostic)
CHARCOT-MARIE-TOOTH DISEASE, AXONAL, TYPE 2E 607684 NEUROFILAMENT PROTEIN, LIGHT POLYPEPTIDE; NEFL 162280 Bristol regional molecular genetics laboratory (Diagnostic)
CHARCOT-MARIE-TOOTH DISEASE, AXONAL, TYPE 2K; CMT2K 607831 GANGLIOSIDE-INDUCED DIFFERENTIATION-ASSOCIATED PROTEIN 1; GDAP1 606598 London Institute of Neurology molecular genetics laboratory (Diagnostic)
CHARCOT-MARIE-TOOTH DISEASE, DEMYELINATING, TYPE 1F 607734 NEUROFILAMENT PROTEIN, LIGHT POLYPEPTIDE; NEFL 162280 Bristol regional molecular genetics laboratory (Diagnostic)
CHARCOT-MARIE-TOOTH DISEASE, TYPE 4A; CMT4A 214400 GANGLIOSIDE-INDUCED DIFFERENTIATION-ASSOCIATED PROTEIN 1; GDAP1 606598 London Institute of Neurology molecular genetics laboratory (Diagnostic)
Charge Syndrome 214800 Chromodomain helicase DNA-binding protein-7; CHD7 608892 Birmingham regional molecular genetics laboratory (Diagnostic) AND Glasgow regional molecular genetics laboratory (Diagnostic)
EPISODIC ATAXIA, TYPE 2; EA2 108500 CALCIUM CHANNEL, VOLTAGE-DEPENDENT, P/Q TYPE, ALPHA 1A SUBUNIT; CACNA1A 601011 Sheffield regional molecular genetics laboratory (Diagnostic)
Fibrodysplasia Ossificans Progressiva; FOP 135100 Activin A, type 1 receptor ; ACVR1 102576 Glasgow regional molecular genetics laboratory (Diagnostic)
Hypertrophic Neuropathy of Dejerine Sottas 145900 Early Growth Response 2; EGR2 129010 Bristol regional molecular genetics laboratory (Diagnostic)
PERIAXIN; PRX 605725
INFANTILE SPASM SYNDROME, X-LINKED 308350 CYCLIN-DEPENDENT KINASE-LIKE 5; CDKL5 300203 Cardiff regional molecular genetics laboratory (Diagnostic)
MIGRAINE, FAMILIAL HEMIPLEGIC, 1; FHM1 141500 CALCIUM CHANNEL, VOLTAGE-DEPENDENT, P/Q TYPE, ALPHA 1A SUBUNIT; CACNA1A 601011 Sheffield regional molecular genetics laboratory (Diagnostic)
NEUROPATHY, CONGENITAL HYPOMYELINATING 605253 Early Growth Response 2; EGR2 129010 Bristol regional molecular genetics laboratory (Diagnostic)
OSTEOGENESIS IMPERFECTA TYPE 3; OI3 259420 COLLAGEN, TYPE 1, ALPHA 1; COL1A1 120150 Sheffield regional molecular genetics laboratory (Diagnostic)
COLLAGEN, TYPE 1, ALPHA 2; COL1A2 120160
RETINITIS PIGMENTOSA; RP 268000 retinitis pigmentosa GTPase regulator; RPGR 312610 Manchester regional molecular genetics laboratory (Diagnostic)
retinitis pigmentosa 2 (X-linked recessive); RP2 312600
rhodopsin (opsin 2, rod pigment) (retinitis pigmentosa 4, autosomal dominant); RHO 180380
peripherin 2 (retinal degeneration, slow); PRPH2 179605
PRP31 pre-mRNA processing factor 31 homolog (S. cerevisiae); PRPF31 606419
PRP8 pre-mRNA processing factor 8 homolog (S. cerevisiae); PRPF8 607300
neural retina leucine zipper; NRL 162080
MP (inosine monophosphate) dehydrogenase 1;IMPDH1 146690
PDGFA associated protein 1; PDAP1 607075
retinitis pigmentosa 1 (autosomal dominant); RP1  
SPASTIC PARAPLEGIA 3, AUTOSOMAL DOMINANT; SPG3A 182600 SPASTIC PARAPLEGIA 3A (AUTOSOMAL DOMINANT); SPG3A 606439 Sheffield regional molecular genetics laboratory (Diagnostic)
Spastic Paraplegia 31, autosomal dominant; SPG31 610250 RECEPTOR EXPRESSION-ENHANCING PROTEIN 1; REEP1 609139 Sheffield regional molecular genetics laboratory (Diagnostic)
Last updated 17-Apr-2008 14:52:02